Congenital tricuspid atresia with transposition of the great vessels.

Congenital tricuspid atresia has been classified into two groups, those with and those without transposition of the great vessels (Kiihne, 1906). Each of these groups is further subdivided according to whether there is an increase or a decrease in the pulmonary blood flow (Edwards and Burchell, 1949). Tricuspid atresia with transposition of the great vessels and an increase in pulmonary blood flow is uncommon and is associated with an average survival time of three months (Keith et al., 1958). We have recently had the opportunity to study three hearts with this defect, one from a boy who survived for five years.